ISBT blood group system

The international Society of Blood Transfusion (ISBT) defines 36 blood group systems. These blood group systems mostly come from variations in glycosylation patterns or from single nucleotide polymorphisms. The table below indicates the protein availability in RESPIRE (R) or a direct link to genecards otherwise (G).

NumberSystem nameSystem SymbolRESPIRE (R) or GeneNames (G)
001ABOABOHisto-blood group ABO system transferase (G)
002MNSMNSGlycophorin-A (R)
Glycophorin-B (G)
003P1PKP1PKAlpha 1,4-galactosyltransferase (P blood group) (G)
004RhRHBlood group Rh(CE) polypeptide (R)
Blood group Rh(D) polypeptide (R)
005LutheranLUBasal cell adhesion molecule (R)
006KellKELKell blood group glycoprotein (R)
007LewisLEFucosyltransferase 3 (Lewis blood group) (G)
008DuffyFYAtypical chemokine receptor 1 (R)
009KiddJKUrea transporter 1 (R)
010DiegoDIBand 3 anion transport protein (R)
011YtYTAcetylcholinesterase (R)
012XgXGXg blood group (G)
013ScianaSCerythroblast membrane associated protein (Scianna blood group) (G)
014DombrockDOEcto-ADP-ribosyltransferase 4 (R)
015ColtonCOAquaporin-1 (R)
016Landsteiner-WienerLWIntercellular adhesion molecule 4 (R)
017Chido/RogersCH/RGComplement C4-A (R)
Complement C4-B (R)
018HHFucosyltransferase 1 (H blood group) (G)
019KxXKMembrane transport protein XK (R)
020GerbichGEGlycophorin-C (R)
021CromerCROMComplement decay-accelerating factor (R)
022KnopsKNComplement receptor type 1 (R)
023IndianINCD44 antigen (R)
024OkOKBasigin (R)
025RaphRAPHCD151 (G)
026John Milton HagenJMHSemaphorin-7A (R)
027IIGlucosaminyl (N-acetyl) transferase 2 (I blood group) (G)
028GlobosideGLOBBeta-1,3-N-acetylgalactosaminyltransferase 1 (globoside blood group) (G)
029GillGILAquaporin 3 (Gill blood group) (G)
030Rg-associated glycoproteinRHAGAmmonium transporter Rh type A (R)
031FORSFORSGloboside alpha-1,3-N-acetylgalactosaminyltransferase 1 (FORS blood group) (G)
032JRJRATP-binding cassette sub-family G member 2 (R)
033LANLANATP-binding cassette sub-family B member 6, mitochondrial (R)
034VelVELSmall integral membrane protein 1 (R)
035CD59CD59CD59 glycoprotein (R)
036AugustineAUGEquilibrative nucleoside transporter 1 (R)